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¹Dr. Lütfi Kırdar Kartal Eğitim ve Araştırma Hastanesi, Radyasyon Onkolojisi Kliniği, İstanbul
²Dr. Lütfi Kırdar Kartal Eğitim ve Araştırma Hastanesi, Patoloji Bölümü, İstanbul Primitive neuroendocrine tumors (PNETs) are rare neoplasms that are usually seen in children and frequently metastasis in the central nervous system. At this setting, intramedullary, extramedullary, intra-extramedullary and extradural have been described. To our knowledge, only 25 cases of purely intramedullary PNETs (IPNETs) have been previously reported. We present a case of primary intrameduller PNET. The initial treatment of the PNET is surgery and, if possible, the radical extirpation of the tumour. Administration of radiotherapy and chemotherapy appears to increase survival. Keywords : Intrameduller primitive neuroendocrine tumor; chemotherapy; radiotherapy